Ọrịa Behcet

Ọrịa Behcet bụ ọrịa na-adịghị ala ala, ọrịa kachasị na Japan na obodo Mediterenian. Ọtụtụ mgbe, ọ na - amalite n'ime ndị dị afọ 30 - 40. Ọrịa a bụ nke òtù vasculitis ma nwee etiology undefined.

Ihe kpatara ọrịa Behcet

Ejikọtara ọrịa ahụ na ọtụtụ ihe ndị na-ebute ọdịnihu, otu n'ime ha bụ:

Ọtụtụ ndị ọkachamara kwenyere na mmalite nke ọrịa Behçet na-akpalite ihe ndị na-efe efe, na n'ọdịnihu, usoro autoimmune na-adakwasị ha, ma ọ bụrụ na a na-ebute ya.

Mgbaàmà nke ọrịa Behcet na ụmụ nwanyị

Ọrịa a bụ polysimptomicity. N'okwu a, ihe ịrịba ama ndị bụ isi, site na nke ị nwere ike ịchọta nchọpụta ziri ezi, jikọtara ya na mmebi nke ụbụrụ mucous nke ọnụ na akụkụ ndị ọzọ, yana usoro mmebi ahụ na anya. Tụlee ihe niile a chọpụtara nke Behçet ọrịa.

Akwụsị akụkụ uzo ọnụ

Na mbido, obere vesicles na ihe igwe ojii na-apụta na egbugbere ọnụ, mbara igwe, ire, gums, pharynx, n'ime ime cheeks, nke na-emeghe meghere. N'ebe nke vesicles, gburugburu, a na-akpụ ụcha na-egbu mgbu (aphthae) nke na-acha odo odo na-egbu maramara, nke nwere ike iru 2 cm n'ịdị elu. Ọgwụgwọ nke nsí na-eme ihe dị ka otu ọnwa gasịrị, na ugboro 3-4 n'afọ, ọnya ahụ na-alọghachi.

Ọrịa nwoke

Ndị inyom na akpụkpọ anụ mucous nke ikpu ma gbasaa na-egbuke egbuke, mgbe ọ na-egbu mgbu, yiri nke na-apụta n'ọnụ. Mgbe o gwusịrị, scars nwere ike ịnọ n'ọnọdụ ha.

Nsogbu nke ọhụụ

Ihe ngosi ndị a na-egosi izu ole na ole mgbaàmà nọ n'oghere ọnụ. Ndị ọrịa nwere ike ịmalite ịmịnye nke iris na ikiri anụ ahụ nke eyeball, mbufụt nke anya anụ ahụ na-egbuke egbuke na nke mucous nke anya, mbufụt nke cornea. Ọtụtụ mgbe, e nwere ihe mgbaàmà ndị a: photophobia, ọhụụ na-ahụ anya, mụbaa lacrimation.

Ihe ngosi mmebi

Erythema nodular, pyoderma, ọkụ-ala-vesicular nwere ike ịpụta. N'ọnọdụ ụfọdụ, a na-ahụ nkwụ ntutu nests, panaritium dị ala.

Nsogbu nke usoro ihe mgbu

Enwere mmepe nke ogbu na nkwonkwo (nke na-agbakarị njedebe) n'enweghị ihe ọghọm na-ebibi.

Mgbaàmà ndị mmadụ

Enwere ihe omimi nke mmekorita akwara, mmepe nke meningoencephalitis, edema nke disiki nerve disiki, ọdịdị nke hemiparesis.

Mmetụta ahụ na-egbuke egbuke na-agbanwe agbanwe

Ihe gbasara mmepe nke vasculitis, thrombophlebitis nke anụ ahụ dị na ụkwụ, thrombosis nke mmiri ọgwụ hepatic na thromboembolism nke artery pulmonary, aortic aneurysm, wdg.

Site na ọnya nke trastrointestinal tract, obi na akpa ume, enwere ike inwe ụdị mgbaàmà ndị a:

Ọgwụgwọ Behcet's Disease

A na-eji ọgwụ Behcet agwọ ọrịa, nke mbụ, iji mee ka ndụ onye ọrịa ahụ dịkwuo ogologo, na-enweta mgbatị dị ogologo oge na igbochi mgbanwe ndị na-enweghị ike ịgbanwe n'ime akụkụ ahụ.

Ngosipụta ugbochi nke Behcet's syndrome na oghere ọnụ na n'akụkụ ndị ahụ na-agbaso ọgwụgwọ mpaghara site na iji glucocorticosteroids , ngwọta antiseptik, na mgbe ụfọdụ - ndị na-egbochi ọgwụ nje. Ọzọkwa maka ọgwụgwọ ọrịa ahụ, ndị na-emepụta cytostatic, immunosuppressors, vitamin nwere ike ịhazi. A na-eji usoro ịwa ahụ eme ihe ọjọọ. A na-eme ka ọtụtụ ndị ọrịa na-ahụ maka hemocorrection extracorporal. A na-agwọ ọgwụgwọ n'okpuru nlekọta ahụ ike mgbe niile.